41. Nephroblastoma nephroblastoma. Three associated congenital malformations 1. WAGR Wilms,aniridia, genital abnormalities, mental retardation (33% risk of tumor). http://pathophysiology.uams.edu/Spring01/peds/lect40-s01/tsld045.htm

Nephroblastoma Three associated congenital malformations: 1. WAGR - Wilms, aniridia, genital abnormalities, mental retardation (33% risk of tumor). An abnormality on chromosome 11p13 (WT-1 a possible tumor suppressor gene). 2. Denys-Drash syndrome - Gonadal dysgenesis (male pseudohermaphroditism) and renal glomerular sclerosis. WT-1. Previous slide Next slide Back to first slide View graphic version

42. Complete List Of MeSH-C Terms Found In References Related To Malignant Hyperthermia 2 Cleft Lip 2 Limb Deformities, congenital 2 Oral andEmbryonal 1 Anus Diseases 1 Aneurysm 1 nephroblastoma 1 Craniofacial http://www.bork.embl-heidelberg.de/g2d/list_mesh_disease.pl?U6589:Smith-Lemli-Op

43. Indian Pediatrics - Editorial The authors had reported various congenital anomalies of the central nervous tumorsoften associated with the BWS such as nephroblastoma, neuroblastoma, rhabdo http://www.indianpediatrics.net/mar2002/mar-299-304.htm

Home Past Issue About IP About IAP ... Subscription Case Reports Indian Pediatrics 2002; 39:299-304 Incomplete Beckwith-Wiedemann Syndrome in a Child with Orbital Rhabdomyosarcoma V. Thavaraj Anitha Sethi* L.S. Arya From the Division of Pediatric Oncology, Department of Pediatrics and *Rajendra Prasad Center for Ophthalmic Sciences, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110 029, India. Correspondence to: Dr. V. Thavaraj, Department of Pediatrics, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110 029, India. E-mail: sowmyam@mantraonline.com Manuscript received: May 31, 2001; Initial review completed: July 18, 2001; Revision accepted: September 5, 2001. Beckwith-Wiedemann syndrome (BWS) was first recognized as a syndrome by Beckwith in 1963, when he reported autopsy findings on three unrelated children with omphalocele, macroglossia, cytomegaly of adrenal cortex, renal medullary hyperplasia and hyperplastic visceromegaly(1). In 1964 Wiedemann published an article on the same syndrome in three siblings with omphalocele, macrosmia and neonatal hypoglycemia(2). The incidence of BWS has been estimated to be 1:13700 live births(3). The increased risk of tumor formation in BWS patients is estimated to be 7.5%(4) and the risk is further increased to 10% if hemihypertrophy is present(4). It has been suggested that BWS can be inherited by the homozygous state of an autosomal recessive mutation(5). We describe a rare case report of partial expression of BWS associated with orbital rhabdomyosarcoma (RMS).

44. MEDLINEplus Medical Encyclopedia: Topics Beginning With N syndrome acute see Acute nephritic syndrome. nephroblastoma see Wilms Nephrogenicdiabetes insipidus - congenital see congenital nephrogenic diabetes insipidus; http://www.nlm.nih.gov/medlineplus/ency/encyclopedia_N.htm

Skip navigation Other encyclopedia topics: A-Ag Ah-Ap Aq-Az B-Bk ... Z Medical Encyclopedia Topics beginning with "N" Na+ see Serum sodium Nabothian cyst Nail abnormalities Nail abnormalities - causes see Brittle nails - causes Nail blanch test see Capillary nail refill test Nail care for newborns Nail polish Nails - fungal infection see Fungal nail infection NALD see Adrenoleukodystrophy Nalfon see Fenoprofen calcium overdose Nalfon overdose Naphthalene Naprosyn overdose Naproxen sodium see Naprosyn overdose Narcissistic personality disorder Narcolepsy Narcotic abuse see Drug abuse Narcotics - screen see Toxicology screen Nasal allergies see Allergic rhinitis Nasal congestion Nasal CPAP Nasal discharge ... Nasal mucosal biopsy Nasal obstruction see Nasal congestion Nasal polyps Nasal septum repair see Septoplasty Nasal tumor see Juvenile angiofibroma Nasopharyngeal culture Natal teeth Natural short sleeper ... Nausea and vomiting Nausea in the morning - females see Morning sickness NBP see Prostatitis - nonbacterial NBT test see Nitroblue tetrazolium test NCV see Nerve conduction velocity Near drowning Nearsightedness Nearsightedness surgery see Corneal surgery Neatsfoot oil NEC see Necrotizing enterocolitis Neck lump Neck pain Neck stiffness see Neck pain Neck X-ray Neck/spinal injury see Spinal/neck injury Necrosis Necrosis - acute tubular see Acute tubular necrosis Necrosis - renal papillae see Renal papillary necrosis Necrosis - renal tubular see Acute tubular necrosis Necrotic see Necrosis Necrotizing colitis see Pseudomembranous colitis Necrotizing enterocolitis Necrotizing fasciitis see

45. Childhood Abdominal Masses Gastrointestinal congenital hypertrophic pyloric stenosis; Crohn's disease; Hydronephrosis;nephroblastoma; Urethral valves. Other Neuroblastoma; Splenomegaly; http://www.surgical-tutor.org.uk/system/hnep/abdominal_masses.htm

Up Tracheostomy Foreign bodies Epistaxis ... Rectal bleeding in childhood [ Childhood abdominal masses ] Choledochal cysts Cryptochidism Paediatric hernias Circumcision ... Neck lumps in children Abdominal masses in children Causes of abdominal masses Gastrointestinal Congenital hypertrophic pyloric stenosis Crohn's disease Intussusception Constipation Liver Biliary atresia Choledochal cysts Hepatitis Hepatoblastoma Genitourinary Hydronephrosis Nephroblastoma Urethral valves Other Neuroblastoma Splenomegaly Retroperitoneal sarcoma Teratoma Nephroblastoma (Wilms' tumour) Originates from the embryonal kidney Pathologically contains renal tissue with various degrees of differentiation Affects about 1 in 10,000 live births 60% present before the age of three years 10% tumours are bilateral The presentation is with an: Abdominal mass (90%) Abdominal pain (20%) Haematuria (30%) Diagnosis can be confirmed by CT scan 40% have metastatic spread at presentation but do not prevent cure Treatment is with nephrectomy and postoperative chemotherapy and radiotherapy Stage 4 disease (haematogenous spread) has 3-year survival less than 30% Neuroblastoma Arises from neural crest tissue - usually adrenal medulla or sympathetic ganglia Show a range of malignancy from benign ganglioneuroma to malignant neuroblastoma Tumours in children are usually malignant 75% are abdominal 25% arise in thorax, pelvis or neck

46. Andrew Arrow Myocarditis Myoclonus Myopathies, Structural, congenital Myopathies, Nemaline Neoplasm,Residual Nephritis, Hereditary nephroblastoma Nephrosis Nephrotic http://andrewarrow.com/writing/diseases1.html

47. Anterior Abdominal Wall - DIAGNOSIS OF CONGENITAL ABNORMALITIES - THE 18-23 WEEK hypoglycemia. About 5% of affected individuals develop tumors during childhood,most commonly nephroblastoma and hepatoblastoma. Prevalence. http://www.centrus.com.br/DiplomaFMF/SeriesFMF/18-23-weeks/chapter-06/abdome_fmf

Anterior Abdominal Walll Handbook of Fetal Abnormalities Algorithms Appendix Anterior abdominal wall Normal Sonography Anatomy Exomphalos Gastroschisis Body Stalk Anomaly ... Authors NORMAL SONOGRAPHIC ANATOMY Normal development of the anterior abdominal wall depends on the fusion of four ectomesodermic folds (cephalic, caudal and two lateral). At 8–10 weeks of gestation, all fetuses demonstrate herniation of the mid-gut that is visualized as a hyperechogenic mass in the base of the umbilical cord; retraction into the abdominal cavity occurs at 10–12 weeks and is completed by 11 weeks and 5 days. The integrity of the abdominal wall should always be demonstrated; this can be achieved by transverse scans demonstrating the insertion of the umbilical cord. It is also important to visualize the urinary bladder within the fetal pelvis, because this rules out exstrophy of the bladder and of the cloaca. EXOMPHALOS Exomphalos results from failure of normal embryonic regression of the mid-gut from the umbilical stalk into the abdominal celom. The abdominal contents, including intestines and liver or spleen covered by a sac of parietal peritoneum and amnion, are herniated into the base of the umbilical cord.

48. Fetal Turmors - DIAGNOSIS OF CONGENITAL ABNORMALITIES - THE 18-23 WEEKS SCAN intrauterine exposure to antithyroid drugs or congenital metabolic disorders the mostfrequent renal tumor, while Wilms’ tumor (nephroblastoma) is extremely http://www.centrus.com.br/DiplomaFMF/SeriesFMF/18-23-weeks/chapter-11/tumors.htm

Fetal Tumors Handbook of Fetal Abnormalities Algorithms Appendix Fetal tumors With the collaboration of Israel Goldstein Introduction Etiology and mechanisms of carcinogenesis Classification Intracranial ... Authors Introduction Etiology and mechanisms of carcinogenesis Developmental errors during embryonic and fetal maturation may result in embryonic tumors. One hypothesis is that more cells are produced than are required for the formation of an organ or tissue and the origins of embryonic tumors rest in developmental errors in these surplus embryonic rudiments. Embryonic tumors developing after infancy are explained by the persistence of cell rests or developmental vestiges. Developmentally anomalous tissue (such as hamartomas and dysgenic gonads) is a source of neoplasms in older children and adults. When any of this developmentally abnormal tissue is present at birth, it is inferred that the cells failed to mature, migrate or differentiate properly during intrauterine life. Benignity of fetal and infantile neoplasms Some neonatal and infantile tumors have a benign clinical behavior despite histological evidence of malignancy. Examples include congenital neuroblastomas and hepatoblastomas in the first year of life, and congenital and infantile fibromatosis, and sacrococcygeal teratomas in the first few months of life. The factors responsible for this ‘oncogenic period of grace’, which starts in utero and extends through the first few months of extrauterine life, are uncertain.

49. Disease Reference syndrome acute nephroblastoma Nephrocalcinosis Nephrogenic diabetes insipidusNephrogenic diabetes insipidus - congenital Nephrolithiasis Nephropathy http://www.pennhealth.com/ency/index/diseidxn.htm

Disease Reference A B C D ... Nutrition - inadequate

50. Ref6 Nucleolar organizer regions in congenital mesoblastic nephroma JFM, Krul EJ, MF T.Mesoblastic nephromas a study of 29 tumors from the SIOP nephroblastoma file http://www.anapath.necker.fr/site/SLMos/SLMos.data/Composants/cases/case06/Ref6.

References 1. Bolande R.P., Brough A.J., Izant R.J. Congenital mesoblastic nephroma of infancy. Pediatrics 1967;40:272-278. 2. Gaillard D., Bouvier R., Sonsino E., et al. Nucleolar organizer regions in congenital mesoblastic nephroma. Pediatric Pathology 1992;12:811-821. 3. Sandstedt B., Delemarre J.F.M., Krul E.J., M.F. T. Mesoblastic nephromas: a study of 29 tumors from the SIOP nephroblastoma file. Histopathology 1985;9:741-750. 4. Howell C.G., Othersen H.B., Kiviat N.E., Norkool P., Beckwith J.B., D'Angio G.J. Therapy and outcome in 51 children with mesoblastic nephroma: a report of the national Wilms'tumor study. J. Pediatr. Surg. 1982;17:826-831. 5. Joshi V.V., Kasznica J., Walters J. Atypical mesoblastic nephroma. Arch. Pathol. Lab. Med. 1986;110:100-106. 6. Bolande R.P. Congenital and infantile neoplasia of the kidney. Lancet 1974;21:1497-1499. 7. Vujanic G.M., Sandstedt B., Dijoud F., Harms D., Delemarre J.F.M. Neprogenic rest associated with mesoblastic nephroma- what does it tell us ? Ped. Pathol. 1994;15:469-475. 8. Bauer J.H., Durham J., Miles J., Hakami N., Gropshong T. Congenital mesoblastic nephroma presenting with primary reninism. Pediatrics 1979;95:268-272.

51. Birth Disorder Information Directory - W Macules, Hereditary congenital Hypopigmented and Hyperpigmented) William('s)(Beuren) Syndrome List of Sites. Wilms Tumor (nephroblastoma) List of Sites; http://www.bdid.com/defectw.htm

HOME W W Syndrome See (Pallister) W Syndrome Waaler Aarskog Syndrome (Hydrocephalus with Costovertebral Dysplasia and Sprengel Anomaly) Waaler aarskog syndrome BASAL CELL NEVUS SYNDROME; BCNS Waardenburg Syndrome List of Sites -(Recessive) Anophthalmia Syndrome See Waardenburg Syndrome, Type III -Shah Syndrome See Waardenburg Syndrome, Type IV with Hirschsprung Disease See Waardenburg Syndrome, Type IV Wagner Syndrome (Erosive Vitreoretinopathy, Hyaloideoretinal Degeneration of Wagner, Wagner Vitreoretinal Degeneration) HYALOIDEORETINAL DEGENERATION OF WAGNER Wagner disease WAGR Syndrome See Wilms Tumor-Aniridia-Genitourinary Anomalies-Mental Retardation (WAGR) Syndrome Walbaum Titran Durieux Crepin Syndrome (Fibular Hypoplasia with Scapulo Pelvic Dysplasia and Absent 5th Fingers) Walbaum titran durieux crepin syndrome Walker Dyson Syndrome (Aniridia-Mental Retardation Syndrome) Aniridia mental retardation syndrome Walker Warburg Syndrome (Cerebroocular Dysgenesis; Cerebroocular Dysplasia-Muscular Dystrophy Syndrome; Chemke Syndrome; COD-MD Syndrome; Hard +/- E Syndrome; H ydrocephalus

52. Www.georgetown.edu/dml/educ/path/lab19/lab19.txt This congenital hydronephrosis was secondary to an atresia of the urethra. 194a4.Wilms' Tumor - nephroblastoma History- This five year old boy was noted http://www.georgetown.edu/dml/educ/path/lab19/lab19.txt

31 [19-1a]: Pediatric Pathology 1. Congenital Cytomegalovirus History- This male infant was noted by ultrasound to have an enlarged abdomen at 24 weeks gestation. The 22- year-old mother gave a history of a brief febrile illness during her first few weeks of pregnancy. The infant was born by spontaneous vaginal delivery at 35 weeks gestation. The infant died shortly after birth of respiratory distress. A. At birth the infant was noted to have an enlarged abdomen with a prominent fluid wave that extended into his enlarged scrotum. Note the numerous petechiae (small hemorrhages) over the trunk, face and limbs. [19-1b]:1B. The abdomen was filled with clear yellow fluid that distended the abdomen, elevating the diaphragms and compressing the developing lungs. The liver was only mildly enlarged. [19-1c]:1C. The liver architecture is distorted by prominent lymphoid aggregates in and adjacent to portal areas. Bile ducts are lined by normal appearing or occasional enlarged epithelial cells. [19-1d]:1D. The enlarged bile duct epithelial cells are 3- 4X the size of the normal cells and contain an enlarged nucleus with a prominent eosinophilic inclusion surrounded by a clear "halo". These cells are pathognomonic of cytomegalovirus infection. [19-1e]:1E. The brain was mildly hydrocephalic with dilated ventricles and a thinned cerebral cortex. Upon sectioning the brain a coarseness was felt in the periventricular region representing areas of calcification. Questions 1. What is the incidence of CMV infection during pregnancy and how many infants will be mildly or severely infected? 2. What are the clinical manifestations of congenital CMV infection? 3. What other organisms are associated with congenital infections? [19-2a]:2. Congenital Group B Streptococcal Infection History- This term male infant was born 28 hours after premature rupture of the amniotic membranes. He was in mild respiratory distress at birth which progressed rapidly to death at 8 hours of age. A. The lungs at autopsy were consolidated and unevenly expanded. [19-2b]:2B. Bronchi, bronchioles and alveolar ducts are filled with acute inflammatory cells (neutrophils). [19-2c]:2C. Alveoli are distended by neutrophils and macrophages along with thin linear eosinophilic structures representing aspirated squamous cells (squames) that are sloughed from the infant's skin after about 25 weeks gestation. Note the faintly basophilic granular material in the alveolus representing clusters of bacteria. [19-2d]:2D. A section from the placenta of this infant displays marked subchorionic inflammation that extends through the chorion into the amnion (acute chorioamnionitis). Questions- 1. What are the routes through which an infant may become infected inutero? 2. How does Group B Streptococcal infection differ from a TORCH infection? 3. Describe the stages or degrees of infection of the placenta? [19-3a]:3. Potter Syndrome History- This term male infant was born to a mother who had been noted to have oligohydramnios throughout the third trimester. The infant experienced severe respiratory distress and died minutes after birth. A. Note the 'cramped' position of the infant with the arms folded across the chest (compressing the thorax) and the legs bent across the abdomen (twisting the feet). [19-3b]:3B. From the side, the typical features of Potter's Facies can be seen including a sloping forehead, flattened nose, recessed chin and lowset floppy ears (elephant-like). [19-3c]:3C. The opened thorax shows a narrow thoracic cavity occupied mainly by the heart, allowing little room for the development of the lungs. [19-3d]:3D. The lungs, while appearing normal in configuration, weigh only 22 grams vs an expected weight of 54 grams for a term infant. [19-3e]:3E. A section from the periphery of the lungs shows a terminal bronchiole just beneath the pleura. A radial alveolar count (RAC) is made by extending a perpendicular line from the center of the bronchiole to the pleura and counting the number of alveolar septa crossed. In a term infant this number is usually 5 or 6 compared to 2 or 3 in this infant. This decreased RAC is indicative of pulmonary hypoplasia. [19-3f]:3F. With the bowel distal to the stomach removed from the abdomen, the vertebral column and adjacent psoas muscles are easily seen. The kidneys, however, are absent, although the adrenals can be seen near the top of the psoas muscles on either side. [19-3g]:G. The surface of the placenta is studded with small white nodules (amnion nodosum) representing collections of amniotic cells stuck to the surface, a frequent finding in cases of oligohydramnios. [19-3h]:H. While the kidneys in this Potter's Syndrome infant are present, they are markedly dilated and filled with fluid. This congenital hydronephrosis was secondary to an atresia of the urethra. Potter's Syndrome Questions- 1. What is the mechanism of development (i.e., the etiology) of Potter's Syndrome? 2. What are the major features of Potter's Syndrome? 3. What renal anomalies are associated with the development of Potters Syndrome? 4. What are some other causes of pulmonary hypoplasia? [19-4a]:4. Wilms' Tumor - Nephroblastoma History- This five year old boy was noted by his pediatrician on routine physical exam to have a mass in the right lower quadrant of his abdomen. A CT scan displayed a mass virtually replacing the right kidney. The left kidney was unremarkable. The mass was resected. A. The mass is composed of encapsulated pale tan, lobulated tissue subdivided by irregular fibrous septa. Note the thin rim of normal kidney at upper right. [19-4b]:4B. The tumor consist of sheets and clusters of 'small round blue cells' separated by bands of fibrous connective tissue. Note the duct-like structures within the 'blastemal' cell clusters. [19-4c]:4C. In some areas the entire tumor is composed of tubular structures . [19-4d]:4D. In other areas mesenchymal components resembling immature fibroblasts predominate. [19-4e]:4E. Within the blastemal area clusters of large, hyperchromatic cells with bizarre mitoses (anaplasia) may be present. [19-4f]:4F. Spread of tumor may be seen along veins in the renal hilus. Questions 1. What are the anomalies and syndromes associated with Wilms' tumor? 2. What are the tissue patterns or cells types noted in Wilms' tumor? 3. What are the good and bad prognostic indicators of Wilms' tumor? [19-5a]:5. Rhabdomyosarcoma History- This 9 year old male complained of constipation, and on physical examination was note to have a large retroperitoneal mass that compressed the rectum. The mass was excised. A. The mass is poorly encapsulated and composed of irregular nodules of tan-white tissue. [19-5b]:5B. On cut section the mass consists of soft, tan tissue subdivided by fibrous septa. [19-5c]:5C. In the embryonal form of rhabdomyosarcoma, the tumor is composed of sheets of round to tapered cells in a rich vascular stroma. [19-5d]:5D. In this embryonal rhabdomyosarcoma, note the elongate cells with 'tails' of granular cytoplasm (strap cells) and plump cells with abundant cytoplasm (rhabdomyoblasts). Cross striations may occasionally be seen in these cells. [19-5e]:5E. The alveolar pattern of rhabdomyosarcoma consists of fibrous septa lined by or covered with 'small round blue cells' that may fill the intervening spaces. [19-5f]:5F. The individual cells of the alveolar form may have eccentric collections of eosinophilic cytoplasm (rhabdomyoblasts). [19-5g]:5G. When arising in a hollow structure (bladder, vagina, bile duct) a rhabdomyosarcoma forms 'grape-like' structures and is referred to as botryoid ( a gross description only). [19-5h]:5H. In a botryoid rhabdomyosarcoma, the embryonal pattern consists of a dense collection of rhabdomyoblasts beneath the normal epithelium of the structure involved. Deeper to the epithelium, the cells are less dense and strap cells with cross striations may be present. Questions- 1. What are the most common sites of involvement of rhabdomyosarcoma in children? 2. What are the two basic tissue patterns of rhabdomyosarcoma in children? 3. What factors influence the prognosis of rhabdomyosarcoma?

53. Revista Española De Patología 1982; 15 (4, Octubre-Diciembre) nephroblastoma. Histologic pattern in relation with the natural history ofthe disease, 337346. I. Peculiarities. II. congenital tumors, 347-363. http://www.repatologia.com/crearficheros/1982_4_en.html

Previous Issue Search General Index Original Frontpage ... Next Issue Index Octubre-Diciembre 1982 Volume 15 Issue 4 Page Introduction Llombart Bosch A Presidente de la SEAP Reviews The management of solid tumors in childhood as an example of the recent development of pediatric clinical oncology Winkler K Clínica Pediátrica Universitaria. Hamburgo. Alemania Palabras Clave: chemotherapy, childhood oncology, solid tumors, radiotherapy Original Articles Anatomic pathology and biological behaviour of solid tumors in childhood Harms D Universidad Christian Albrechts. Kiel. R.F. Alemania Palabras Clave: pediatric oncology, teratomas, embryonal tumors, neuroblastoma, nephroblastoma Nephroblastoma. Histologic pattern in relation with the natural history of the disease Contreras F, Picazo MªL, Suárez A Ciudad Sanitaria "La Paz". Madrid Childhood tumors of the central nervous system. I. Peculiarities. II. Congenital tumors Cusi Sánchez V, Vila Torres J, Royo Sanz C Hospital Infantil San Juan de Dios de Barcelona Palabras Clave: brain tumors in infancy, congenital tumors, calcifications

54. ICON Health Publications -- Home Page lymphoma hodgkin's, child malignant lymphoma, child nephroblastoma, child rhabdosarcoma atrophy,cirrhosis of the liver, cirrhosis, congenital pigmentary, clam http://www.icongrouponline.com/health/healthC.html

ICON Health Publications Official Health Sourcebooks Conditions or Treatments A B C D ... Z Search: C. PNEUMONIAE CALCIFYING TENDINITIS OF SHOULDER CAMPYLOBACTER ENTERITIS CANCER - BRAIN TUMOR (PRIMARY) related to CHILDHOOD CEREBRAL ASTROCYTOMA CANCER - BRAIN TUMOR (PRIMARY) related to CHILDHOOD EPENDYMOMA CANCER ACUTE CHILDHOOD LEUKEMIA CANCER BRAIN TUMOR CANCER BREAST related to BREAST CANCER CANCER BREAST related to MALE BREAST CANCER CANCER BREAST related to MATERNAL BREAST CANCER CANCER CERVIX CANCER COLON CANCER ESOPHAGUS CANCER HODGKIN'S LYMPHOMA related to ADULT HODGKIN'S DISEASE CANCER HODGKIN'S LYMPHOMA related to AIDS-RELATED LYMPHOMA CANCER HODGKIN'S LYMPHOMA related to CHILDHOOD HODGKIN'S DISEASE CANCER HODGKIN'S LYMPHOMA related to HODGKIN'S DISEASE DURING PREGNANCY CANCER INTESTINE CANCER KIDNEY related to RENAL CELL CANCER CANCER KIDNEY related to TRANSITIONAL CELL CANCER OF THE RENAL PELVIS AND URETER CANCER KIDNEY OR URETER CANCER LIVER CANCER MESOTHELIOMA CANCER MOUTH ... CANCER NON-HODGKIN'S LYMPHOMA related to ADULT NON-HODGKIN'S LYMPHOMA CANCER NON-HODGKIN'S LYMPHOMA related to CHILDHOOD NON-HODGKIN'S LYMPHOMA CANCER NON-HODGKIN'S LYMPHOMA related to NON-HODGKIN'S LYMPHOMA DURING PREGNANCY CANCER NON-HODGKIN'S LYMPHOMA PREGNANCY CANCER OF LARYNX CANCER OF THE ANUS CANCER OF THE COLON ... CANCER OVARIES related to OVARIAN EPITHELIAL CANCER CANCER OVARIES related to OVARIAN GERM CELL TUMORS CANCER OVARIES related to OVARIAN LOW MALIGNANT POTENTIAL TUMORS CANCER PANCREAS CANCER PROSTATE CANCER RENAL PELVIS OR URETER CANCER SKIN BASAL CELL ... CANCER VAGINA related to EXTRAGONADAL GERM CELL TUMORS

55. FamilyFun: Health Encyclopedia: Wilm's Tumor nephroblastoma, also known as Wilms' tumor, is the most common kidney cancer in Oneof six children who develop the malignancy has congenital deformities of http://familyfun.go.com/raisingkids/child/health/childhealth/dony89enc_wilm/

Search FamilyFun shortcuts Parenting Tools Field Guide to Parenting Parent Problem Solver Pregnancy Calendar Baby Name Finder ... Article Library Parenting Checklists Immunizations Nursery Planner Holidays All Checklists Parenting Experts Jan Faull, Child Development Dominic Cappello, Learning All Experts parent ... to parent Get tips, support Parenting Boards Expecting Potty Training Sleep Stay-at-Home Moms ... E-Cards Creative. Fun. Free. Catching up is easy to do. Send an E-Card WILMS' TUMOR Nephroblastoma, also known as Wilms' tumor, is the most common kidney cancer in children. The tumor usually appears in children less than five years of age (the median age is three), although it may develop in adolescence. Wilms' tumor is about 90 percent curable. Even if the cancer has spread to distant organs, more than half of all patients survive. WHAT CAUSES WILMS' TUMOR? The tumor sometimes runs in families, indicating a genetic influence yet to be defined. One of six children who develop the malignancy has congenital deformities of the urinary tract of the genitals (such as a malformation of the urethra or an undescended testicle ). Other associated abnormalities include structural deformities of the heart and absence of the iris from the eye. Wilms' tumor sometimes develops in a child who has relatives with these congenital abnormalities.

56. UNSW Embryology-OMIM WILMS TUMOR 1 nephroblastoma. The syndrome of aniridia, hemihypertrophy and other congenital anomalieswith Wilms tumor, subsequently known as the WAGR syndrome, was first http://anatomy.med.unsw.edu.au/cbl/embryo/OMIMfind/kidney/OMIM-194070.htm

UNSW Embryology DEVELOPMENT OF THE URINARY SYSTEM Embryology Home Page WILMS TUMOR 1 Select Entry from OMIM Online Mendelian Inheritance in Man (Internet Link) This page is for computers without external internet access. Back to UNSW Embryology-Kidney Notes List of OMIM search results *194070 WILMS TUMOR 1; WT1 Alternative titles; symbols NEPHROBLASTOMA TABLE OF CONTENTS TEXT ALLELIC VARIANTS View List of allelic variants REFERENCES ... "Coriell Cell Line Repository" Gene Map Locus: Note: pressing the symbol will find the citations in MEDLINE whose text most closely matches the text of the preceding OMIM paragraph, using the Entrez MEDLINE neighboring function. TEXT Rather numerous instances of multiple sibs with Wilms tumor have been described ( Fitzgerald and Hardin, 1955

57. ÅÔÁÉÑÅÉÁ ÉÁÔÑÉÊÙÍ ÓÐÏÕÄÙÍ - ÂÇÔÁ ÉÁÔÑÉÊÅÓ Å� ABSTRACT nephroblastoma or Wilms' tumor accounts for most childhood renal neoplasms featureof Wilms' tumor is its association with congenital anomalies (eg http://www.mednet.gr/beta/98-8.htm

PUBLISHED MONTHLY BY THE SOCIETY FOR MEDICAL STUDIES AUGUST 1998 VOLUME 74 No 2 Nephroblastoma of childhood J.P. Panagiotou, S. Polychronopoulou-Androulakakis Dept. of Pediatric Hematology-Oncology, "Aghia Sophia" Children's Hospital, Athens, Greece ABSTRACT Key words Nephroblastoma, childhood. Organization, writing and delivery of an oral scientific presentation J.K. Triantafillidis Dept. of Gastroenterology "Saint Panteleimon" General State Hospital, Nicea, Greece ABSTRACT Key words Lecture, slides, scientific presentation. Syndromes of childhood osteoporosis N. Mygdakos, N.C. Vamvakopoulos Dept. of Biology and Genetics, Larisa University, School of Medicine, Larisa, Greece ABSTRACT Childhood osteoporosis is a rather rare disease affecting normal bone growth, development and homeostasis. This review summarizes the most common diagnostic methods, symptomatology, complications and genetic and other etiologic predisposing factors of the disease. In addition, it is well known that various endocrine and metabolic diseases contribute to the development of childhood osteoporosis. In this respect, their specific therapeutic correction appears to result in the proper management of osteoporotic symptoms, as well. While hormone replacement therapy in hormone deficient children can effectively prevent osteoporosis, equally effective therapeutic approaches for the other forms of the disease are presently lacking. Future advances in biomedicine, including the use of growth factors and somatic cell gene therapy, may help ameliorate or extinguish the devastating effects of this highly debilitating disease.

58. Service Page - Pathologie Information nephroblastoma or Wilms tumor is the most frequent renal tumor in children nephroblastomasmay be associated with a variety of congenital malformations (aniridia http://orphanet.infobiogen.fr/Site/Exp.stm?Lng=GB&Expert=654

59. ORPHANET® : Base De Données Sur Les Maladies Rares Et Les Médicaments Orpheli renal ultrasonography should be performed, looking for nephroblastoma, in any of proteinuriait typically less severe than in congenital nephrotic syndrome of http://orphanet.infobiogen.fr/data/patho/GB/uk-Drash.html

Denys-Drash syndrome Author: Professor Patrick NIAUDET, MD (member of the European editorial committee of Orphanet Encyclopedia) Creation date: October 2001 Disease name and synonyms Diagnosis Criteria/ Definition Incidence Clinical description ... References Disease name and synonyms Denys-Drash syndrome Drash syndrome Wilm's tumor and pseudohermaphroditism Nephropathy, Wilm's tumor and genital anomalies Diagnosis Criteria/ Definition Denys et al. and Drash et al. were the first to report the triad of progressive renal disease, male pseudohermaphroditism and Wilms' tumor [1,2]. All of the patients were infants with severe proteinuria progressing rapidly to renal failure. Incomplete forms of the syndrome were described and the glomerulopathy was identified as diffuse mesangial sclerosis (DMS) [3]. During the early stages, the glomerular lesions are characterized by a high amount of fibrils in the mesangial matrix without mesangial cell proliferation [4-6]. The capillary walls are lined with hypertrophied podocytes. The fully developed lesion consists of thickened glomerular basement membranes associated with massive enlargement of mesangial areas, leading to the reduction of the capillary lumens. Mesangial sclerosis eventually contracts the glomerular tuft into a sclerotic mass within a dilated urinary space. There is usually a corticomedullary gradient of involvement, with the most central glomeruli being less affected. Tubules are severely damaged, especially in the deeper cortex, where they are markedly dilated and often contain hyaline casts.

60. PaediatricNursing Paper I & II syndromes, UTI/Renal failure, obstructive uropathy, congenital defects hynospadis Lymphomes,bleeding disorders, brain tumour, nephroblastoma, bonetumuours. http://www.tnpsc.org/PaediatricNurspg1.htm

SYLLABUS PAEDIATRIC NURSING CLINICAL SPECIALITY POST GRADUATE DEGREE STANDARD PAPER -I code 088 UNIT I INTRODUCTION: Trends in Paediatric and Child health Historical development of Child health Concepts in Child Health Parameter of Child Health Determinants of Child Health National Policy's and laws in Child Health UNIT II PRENATAL PAEDIATRICS Genetics - Theory Genetics - Heredity Genetics - Patterns of disorder Genetics Counselling Prenatal development and care UNIT III NEONATOLOGY Normal newborn physiology Characteristics of newborn Assessment of newborn Care of Newborn High risk neonate Preterm Low birth weight Post term babies PROBLEMS IN NEW BORN Birth Injuries Asphyxia neonatorum Neonatal infections Neonatal Jaundice Neonatal Convulsions Metabolic disorders Neonatal intensive care unit Organization Facilities Available Services offered UNIT IV GROWTH AND DEVELOPMENT Factors of growth and development Theories Laws Principles Concepts Psychosocial development, Cognitive Development

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